A nationwide survey of patients with Bickerstaff brainstem encephalitis: Diversity of underlying mechanism
نویسندگان
چکیده
منابع مشابه
[A nationwide survey of patients with Bickerstaff brainstem encephalitis: diversity of underlying mechanism].
Bickerstaff brainstem encephalitis (BBE) is characterized by acutely progressive bilateral ophthalmoparesis and ataxia with impaired consciousness or pyramidal signs, or both; all of which are followed by a monophasic course with good recovery. Alike Guillain-Barré syndrome (GBS), BBE is proposed to have an autoimmune mechanism triggered by antecedent infection. The nationwide epidemiologic sur...
متن کاملRecurrent Diplopia in a Pediatric Patient with Bickerstaff Brainstem Encephalitis
Introduction. Acute complete external ophthalmoplegia is a rare finding in clinical practice that is associated with diseases affecting the neuromuscular junction, the oculomotor nerves, or the brainstem. Ophthalmoplegia has been reported with acute ataxia in Miller Fisher syndrome (MFS) and Bickerstaff brainstem encephalitis (BBE). Up to 95% of these cases are associated with anti-GQ1b antibod...
متن کاملA Case of Bickerstaff Brainstem Encephalitis and Acute Lymphoblastic Leukaemia
Bickerstaff Brainstem Encephalitis (BBE) is a post-infectious immune disorder. It is rare, yet the most severe variant of Guillain-Barre Syndrome (GBS) in terms of initial presentation. Moreover, the coexistence of BBE and Acute Lymphoblastic Leukaemia (ALL) is distinctly uncommon. We report a case of a patient with a background history of Precursor B cell Acute Lymphoblastic Leukaemia (pre B A...
متن کاملAn elderly patient with Bickerstaff brainstem encephalitis and transient episodes of brainstem dysfunction.
BACKGROUND Bickerstaff brainstem encephalitis (BBE) is a rare inflammatory, demyelinating disease that generally has a good prognosis. OBJECTIVE To describe the course of a patient with severe BBE and multiple medical complications. DESIGN Case report. SETTING Academic medical center. PATIENT An 81-year-old woman with BBE who fully recovered. The patient had transient and very frequent ...
متن کاملBickerstaff brainstem encephalitis and Fisher syndrome: anti-GQ1b antibody syndrome.
In the 1950s, Bickerstaff and Fisher independently described cases with a unique presentation of ophthalmoplegia and ataxia. The neurological features were typically preceded by an antecedent infection and the majority of patients made a spontaneous recovery. In the cases with Bickerstaff brainstem encephalitis, there was associated altered consciousness and in some, hyperreflexia, in support o...
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ژورنال
عنوان ژورنال: Rinsho Shinkeigaku
سال: 2013
ISSN: 0009-918X,1882-0654
DOI: 10.5692/clinicalneurol.53.1322